Primary leiomyosarcoma of the kidney

SummaryPrimary leiomyosarcoma of the kidney is an extremely rare disease. No single case of primary renal leiomyosarcoma was reported at National Taiwan University Hospital during 1995–2010. Here, we report the case of a 74-year-old woman who presented with intermittent lower abdominal pain for 2 months. A heterogeneous tumor was found in the left kidney. The clinical presentation suggested renal cell carcinoma. A diagnosis of leiomyosarcoma was made based on the pathological examination. The patient underwent radical nephrectomy. No distant metastasis was noted. No adjuvant chemotherapy or radiotherapy was provided after surgery