702-1 Long-term (28-Year) Follow-up of Mustard Repair for Transposition of the Great Arteries with Intact Ventricular Septum: Freedom from Right Ventricular (Systemic) Heart Failure

113 30-day survivors of the Mustard repair undertaken between 1964 and 1982 were followed by serial cardiological review and a recent symptom questionnaire. Follow-up of late survivors was 10–28 years; 40 survive >20 years postoperatively. Right ventricular failure (RVF) was diagnosed if there were clinical signs and/or supportive radiological, echocardiographic or radionuclide evidence of progressive right heart dysfunction. Non-progressive RV dilatation was labelled RV dysfunction.ResultsActuarial survival was 93%, 90%, 84%, 80% and 80% at 5, 10, 15, 20 and 24 years respectively. Causes of the 19 deaths were: baffle obstruction 4; sudden, presumed arrhythmia 6; pulmonary vascular disease 2; miscellaneous 5; and RVF 2.Although RV dysfunction is frequently observed, actuarial freedom from RVF is 97% at 18 years.ConclusionProgressive right ventricular failure is rare following the Mustard operation for simple transposition with intact septum