SummaryThe mucopolysaccharidoses are comprised of hereditary disorders joined by errant degradation of mucopolysaccharides. The relatively infrequent opportunity to care for these patients is evidenced by a fairly small number of case reports and anecdotal information. Though lifespan is increasing, onset of respiratory pathology or involvement remains portentous. We present two cases that punctuate the need for insightful decision making while managing the airway for these patient
Background. Treatment of tracheostenosis after tracheostomy in pediatric patients is often difficult...
Mucopolysaccharidoses (MPSs) are lysosomal storage disorders caused by deficiency of enzymes involve...
Abstract The mucopolysaccharidoses (MPS) are a heterogeneous group of inherited metabolic disorders,...
SummaryThe mucopolysaccharidoses are comprised of hereditary disorders joined by errant degradation ...
Introduction: Mucopolysaccharidoses (MPSs) are a group of heredity storage diseases, transmitted in ...
(1) Background: Mucopolysaccharidoses (MPS) are a heterogeneous group of lysosomal storage disorders...
Supplementary Information. Preoperative assessment.BACKGROUND : Mucopolysaccharidoses (MPS) are rare...
This paper provides a detailed overview and discussion of anaesthesia in patients with mucopolysacch...
Abstract This paper provides a detailed overview and dis-cussion of anaesthesia in patients with muc...
Abstract Background Patients suffering from mucopolysaccharidosis are among the most complex from th...
Morquio A syndrome (mucopolysaccharidosis IVA, MPS IVA) is a lysosomal storage disease caused by a d...
Item does not contain fulltextOBJECTIVE: To assess the CT findings of the airway in children with mu...
Airway management for patients with craniofacial abnormalities poses many challenges. It potentially...
Background: Mucopolysaccharidosis type II (MPSII) patients frequently suffer from dyspnoea caused by...
Morquio syndrome (MS) or mucopolysaccharidosis (MPS) type IVA is a progressive lysosomal storage dis...
Background. Treatment of tracheostenosis after tracheostomy in pediatric patients is often difficult...
Mucopolysaccharidoses (MPSs) are lysosomal storage disorders caused by deficiency of enzymes involve...
Abstract The mucopolysaccharidoses (MPS) are a heterogeneous group of inherited metabolic disorders,...
SummaryThe mucopolysaccharidoses are comprised of hereditary disorders joined by errant degradation ...
Introduction: Mucopolysaccharidoses (MPSs) are a group of heredity storage diseases, transmitted in ...
(1) Background: Mucopolysaccharidoses (MPS) are a heterogeneous group of lysosomal storage disorders...
Supplementary Information. Preoperative assessment.BACKGROUND : Mucopolysaccharidoses (MPS) are rare...
This paper provides a detailed overview and discussion of anaesthesia in patients with mucopolysacch...
Abstract This paper provides a detailed overview and dis-cussion of anaesthesia in patients with muc...
Abstract Background Patients suffering from mucopolysaccharidosis are among the most complex from th...
Morquio A syndrome (mucopolysaccharidosis IVA, MPS IVA) is a lysosomal storage disease caused by a d...
Item does not contain fulltextOBJECTIVE: To assess the CT findings of the airway in children with mu...
Airway management for patients with craniofacial abnormalities poses many challenges. It potentially...
Background: Mucopolysaccharidosis type II (MPSII) patients frequently suffer from dyspnoea caused by...
Morquio syndrome (MS) or mucopolysaccharidosis (MPS) type IVA is a progressive lysosomal storage dis...
Background. Treatment of tracheostenosis after tracheostomy in pediatric patients is often difficult...
Mucopolysaccharidoses (MPSs) are lysosomal storage disorders caused by deficiency of enzymes involve...
Abstract The mucopolysaccharidoses (MPS) are a heterogeneous group of inherited metabolic disorders,...