Isolated Dysplasia Epiphysealis Hemimelica of the Hip Joint

Dysplasia epiphysealis hemimelica was first reported as tarsom#{233}galie by Mouchet and Belot in 1926. In 1950, Trevor reported the cases of ten patients, calling the lesion tarsoepiphyseal aclasis, and Fairbank described fourteen ad-additional epiphysis, with the characteristic medial or lateral distribution. The purpose ofthis paper is to report an atypical case of dysplasia epiphysealis hemimelica in a patient who had involvement of the entire capital femoral epiphysis and FIG. 1 Radiograph demonstrating subluxation of the right capital femoral epiphysis secondary to a mass occupying the right acetabulum. There are scattered areas of sclerosis, as well as flattening and fragmentation of the epiphysis. ditional cases in 1956. Fewer than 100 cases seem to have been reported in the literature to date7. Involvement of an entire epiphysis in this rare disorder has been described239’2’6, but always in the presence of an * No benefits in any form have been received or will be received from a commercial party related directly or indirectly to the subject ofthis article. No funds were received in support of this study