DOPA RESPONSIVE DYSTONIA: A CASE REPORT MOHAMMAD GHOFRANI, * M.D., AND

Dopa responsive dystonia (DRD) is a dystonic syndrome of childhood, usually affecting gait and subsequently developing into parkinsonism with a dramatic therapeutic response to levodopa. At the best of our recollection this is the first case in Iranian medical literature of a 13 year old boy, affected by this interesting, rare and treatable disease which can be easily diagnosed if clinicians have a high index of suspicion. We also have a brief discussion on the pathophysiology ofDRD. MJ1R1, Vol. 13, No.3, 235-236,199