CARDIOPATHIES CONGENITALES ET MALFORMATIONS EXTRACARDIAQUES ASSOCIEES

The incidence of various congenital malformations was established in a series of 1,628 autopsies of children aged from 0 to 15 yr. There were 21.3% still borns, 31.7% new borns less than 8 days old and 47% children from 8 days to 15 yr old. The incidence of congenital malformations was found to be 19.9%; the highest frequency was found in the group of older children (24.7%). In 176 cases (10.8%), one or more cardiac anomalies were present. Extracardiac malformations were found in 198 children (12.1%). The most common abnormalities occurred in the genito urinary system (4.6%), central nervous (3.9%), gastro intestinal (3.1%) and skeletal systems (3.1%). Congenital heart disease was associated with other congenital anomalies in 50 cases (28%). The most common association was found with the genito urinary system: 11.4% of the cardiac cases had a urinary tract abnormality, whereas 26.3% of the urological anomalies were associated with various types of cardiac malformations. The cases in which there was only a septal defect (atrial and or ventricular) had the highest incidence of extra cardiac anomalies. These associations were much rarer in cases of complex cardiac anomalies.SCOPUS: NotDefined.j