50. Hospital-Based Frequencies of Primary Vasculitides at Eastern Mediterranean: A Longitidunal Analysis at 7th year

Background: Primary vasculitides are very rare diseases and distribution of vasculitides differ according to geographic region. Since October 2014, vasculitis patients diagnosed in any departments of Hacettepe University Hospitals are prospectively recorded in University Vasculitis Research Centre (HUVAC) database. Distribution of patients at 2nd year was presented in 2017. This study is aimed to report the 7th year results and to compare with them with 2nd year data. Methods: All patients are re-evaluated according to the 2012 revised Chapel Hill nomenclature criteria. Pediatric patients fulfilled the Ankara 2008 criteria for the respective childhood vasculitis. Electronic patient records are periodically searched for the possible vasculitis patients having any of the 10th revision of the International Statistical Classification of Diseases (ICD-10) code for the particular vasculitides. Recently we are also recording vasculitis mimickers. Results: A total of 2464 patients were recruited until 24th November 2021. 514 (20.9%) of them were pediatric patients. The most frequently seen vasculitis among adult patients was Behcet's Disease whereas in pediatric patients it was HSP/IgA Vasculitis (Table). Granulomatous polyangiitis (GPA) was the most common small vessel vasculitis in adults. Takayasu arteritis was more frequent than giant cell arteritis among the adult patients. No differences was found in the comparison of distribution of vasculitides 2nd year with 7th year (p>0.05 for all). Conclusions: Distribution of vasculitides at 2nd and 7th year was similar. Thus we suggest that this is a true reflection of vasculitides in our country. Behcet's Disease is the most frequent vasculitis as expected. However, Takayasu arteritis is more common than GCA in adult patients. GPA is the most common small vessel vasculitis in adulthood. IgA vasculitis and Kawasaki’s disease were frequently seen paediatric vasculitis. Disclosures: No disclosures related to this abstract