Intracystic Papillary Carcinoma in a Male as a Rare Presentation of Breast Cancer: a Case Report and Literature Review

INTRODUCTION: The term intracystic papillary ductal carcinoma in situ has recently changed and is now more appropriately referred to intracystic papillary carcinoma . Intracystic papillary carcinoma in men is an extremely rare disease with only a few case presentations published in the literature so far. CASE PRESENTATION: We discuss a case of a 44-year-old Caucasian man with an intracystic papillary carcinoma treated with simple mastectomy, sentinel lymph-node biopsy and contralateral risk-reducing mastectomy. These were followed by adjuvant radiotherapy of the breast. CONCLUSION: Triple assessment (i.e. clinical examination and radiological and histological assessment) with a high level of clinical suspicion is necessary to diagnose intracystic papillary carcinoma in men due to its rarity. Furthermore, genetic testing and risk-reducing mastectomy should also be considered in cases of a strong family history for male breast cancer