Pulmonary Artery Atresia

Introduction: Pulmonary atresia is a congenital malformation of the heart, a valve in which the pulmonary valve orifice fails to develop. The valve is completely closed thereby obstructing the outflow of blood from the heart to the lungs. Doctors are unsure of the cause of congenital heart defects, but there are some medical conditions that have been found to increase the risk of having a baby with a heart defect such as congenital heart disease in the mother, father, brother, or sister of the baby, a diabetic mother, use of drugs or alcohol or over the counter prescriptions during pregnancy. There are many different types of classification of PA but more useful is a classification in PA with and without interventricular defect. The aim of presentation is to present neonates with pulmonary atresia, with or without interventricular defect in a group of children with central cyanosis and possibility to make a diagnosis of PA with echocardiographic examinations. Methodology: Retrospectively we analyzed children with central cyanosis where etiology of cyanosis where any congenital heart defect. Results: During the period 2008 – 2013 in Pediatric Clinic in Prishtina 28 neonates with PA were diagnosed. Of the, 19 were with an interventricular defect and 9 without. In a group of neonates with PA and without DIV communication at the trial level was restrictive in 8 of them and in 4 balloon atrioseptostomy procedure was successfully performed. 5 of remaining has died, in absent of the possibility for palliative surgical intervention