Retroperitoneal desmoid tumor in a patient with familial adenomatous polyposis: A case report
- Fathia Aidid, MD
- Narjisse Aichouni, MD
- Ihssane Afilal, MD
- Widad Abbou, MD
- Rachid Jabi, MD
- Nadir Miry, MD
- Amal Bennani, MD
- Imane Kamaoui, MD
- Siham Nasri, MD
- Imane Skiker, MD
DOIAbstract
Desmoid tumors are benign fibroblastic neoplasms, with locally invasive features and a tendency of recurrence. They are considered an aggressive non-metastatic fibromatosis. The retroperitoneal location is extremely rare. Their exact mechanism of occurrence is still controversial, but could be related to a genetic predisposition, hormonal factors or traumatic factors, including surgery. This entity faces management difficulties due to its rarity, the variable circumstances of its discovery, and the non-specific clinical manifestations. Their sensitivity to chemotherapy and radiotherapy is limited and surgery remains the only curative treatment in symptomatic cases, however observational waiting could consist the most appropriate management ...
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