A Paraurethral Aggressive (Deep) Angiomyxoma

Background: Aggressive angiomyxomas (AAs) are rare mesenchymal tumors that are histologically composed of myxoid stroma and vasculature. AAs are typically located in the pelvis and perineum and occur more frequently in females of reproductive age. Although a complete resection of the AA is the definitive cure, it is often difficult to achieve due to a lack of capsule in the tumor. Case Presentation: In this report, we outline a patient who had a paraurethral tumor for eight months before symptoms were observed. The mass measured 3.55 cm x 2.0 cm x 1.5 cm and was excised in the operating room under general anesthesia. The histopathology described the mass as a circumscribed hypocellular lesion with myxoid stroma and abundant vasculature, consistent with the diagnosis of aggressive angiomyxoma. The patient’s postoperative course was uneventful, and her symptoms improved within four days of tumor excision. The patient was advised to continue close follow-up with her gynecologist and endocrinologist to monitor for recurrence. Conclusion: Aggressive angiomyxoma is six times more prevalent in females of reproductive age than in males. Due to its rarity, AAs are often misdiagnosed as cysts, hernias, lipomas, or cancerous lesions. Although most cases of AAs are benign, close follow-ups are crucial to monitor for recurrences or metastasis