Interstitial lung disease (ILD) in systemic sclerosis (SSc) is a major cause of morbidity and mortality, mostly presenting as nonspecific interstitial pneumonia. Little is known about the prevalence of pleuroparenchymal fibroelastosis (PPFE), a specific entity affecting the visceral pleura and subpleural parenchyma. We set out to estimate PPFE prevalence in two large cohorts of SSc patients and to assess its impact on survival and functional decline.A total of 359 SSc patients, derived from two referral centers in two different countries (UK and Italy), were included. The first available high-resolution computed tomography scan was independently evaluated by two radiologists blind to clinical information, to quantify ILD extent, freestandin...
In systemic sclerosis (SSc), interstitial lung disease (ILD) is common (>80%) and worsens the pro...
Aurore Bergamasco,1 Nadine Hartmann,2 Laura Wallace,3 Patrice Verpillat41YolaRx Consultants, Paris, ...
Objectives: The epidemiology of interstitial lung disease (ILD) in systemic sclerosis (SSc) in Belgi...
Interstitial lung disease (ILD) in systemic sclerosis (SSc) is a major cause of morbidity and mortal...
Pleuroparenchymal fibroelastosis (PPFE) is a rare new interstitial lung disease (ILD) characterized ...
Abstract Background Pleuroparenchymal fibroelastosis (PPFE) is a very rare interstitial lung disease...
Background: Krebs von den Lungen-6 (KL-6) is a high-molecular-weight (200kDa) glycoprotein proposed ...
Rationale: Interstitial lung disease (ILD) represents a major challenge in systemic sclerosis (SSc),...
Systemic sclerosis (SSc) is a connective tissue disease characterised by fibrosis of the skin and in...
Pleuroparenchymal fibroelastosis (PPFE) is now a defined clinicopathologic entity in the updated 201...
The epidemiology of interstitial lung disease (ILD) in systemic sclerosis (SSc) in Belgium is unknow...
Interstitial lung disease is a relatively frequent manifestation of systemic sclerosis with approxim...
Pleuroparenchymal fibroelastosis (PPFE) is a rare form of interstitial pneumonia, characterized by ...
In systemic sclerosis (SSc), interstitial lung disease (ILD) is common (>80%) and worsens the pro...
Aurore Bergamasco,1 Nadine Hartmann,2 Laura Wallace,3 Patrice Verpillat41YolaRx Consultants, Paris, ...
Objectives: The epidemiology of interstitial lung disease (ILD) in systemic sclerosis (SSc) in Belgi...
Interstitial lung disease (ILD) in systemic sclerosis (SSc) is a major cause of morbidity and mortal...
Pleuroparenchymal fibroelastosis (PPFE) is a rare new interstitial lung disease (ILD) characterized ...
Abstract Background Pleuroparenchymal fibroelastosis (PPFE) is a very rare interstitial lung disease...
Background: Krebs von den Lungen-6 (KL-6) is a high-molecular-weight (200kDa) glycoprotein proposed ...
Rationale: Interstitial lung disease (ILD) represents a major challenge in systemic sclerosis (SSc),...
Systemic sclerosis (SSc) is a connective tissue disease characterised by fibrosis of the skin and in...
Pleuroparenchymal fibroelastosis (PPFE) is now a defined clinicopathologic entity in the updated 201...
The epidemiology of interstitial lung disease (ILD) in systemic sclerosis (SSc) in Belgium is unknow...
Interstitial lung disease is a relatively frequent manifestation of systemic sclerosis with approxim...
Pleuroparenchymal fibroelastosis (PPFE) is a rare form of interstitial pneumonia, characterized by ...
In systemic sclerosis (SSc), interstitial lung disease (ILD) is common (>80%) and worsens the pro...
Aurore Bergamasco,1 Nadine Hartmann,2 Laura Wallace,3 Patrice Verpillat41YolaRx Consultants, Paris, ...
Objectives: The epidemiology of interstitial lung disease (ILD) in systemic sclerosis (SSc) in Belgi...