Bilateral lens capsule rupture in a patient with previously undiagnosed Alport’s syndrome

Background: The purpose of this paper was to report a case of bilateral lens capsule rupture in a patient withpreviously undiagnosed Alport’s syndrome. Case presentation: A 12-years-old child was referred to our hospital for cataract extraction secondary to decreased visual acuity in the right eye two years after lensectomy and posterior chamber intraocular lens implant in the left eye secondary to assumed traumatic cataract. Slit-lamp examination showed a ruptured anterior capsule in the right eye with lens matter in the anterior chamber. Clinically the patient was anemic and deaf; he was referred for pediatric evaluation and was diagnosed with Alport’s syndrome and end-stage renal disease. Once the patient’s hypertension was controlled, a lensectomy and posterior chamber intraocular lens implant was performed. Results: Lensectomy and posterior chamber intraocular lens implant removed the cataract and allowed the restorationof visual acuity. Conclusions: Ophthalmologists may be the first to consider the diagnosis of Alport’s syndrome based on lenschanges. Uncontrolled Blood pressure can delay surgery, during which time intraocular pressure (IOP) should bemonitored closely. Results of lensectomies with foldable IOL implantation are successful. To our knowledge, thisis the second report of a case of bilateral lens capsule rupture in a patient with previously undiagnosed Alport’ssyndrome