Badbak-distribusie van Lamellere Igtiose die Bantoe

An unusual distribution of lamellar ichthyosis in 13 Black patients from 9 families is described. The trunk and upper extremities were mainly affected. In all patients, the temples were affected to a greater or lesser degree. The skin of the face, lower extremities, hands and feet was normal. In 1 patient the entire forehead was affected, and the skin of the upper and lower extremities showed patchy ichthyotic changes. Histologically and electron-microscopically, the picture is similar to that of lamellar ichthyosis (non-bullous congenital ichthyosiform erythroderma). Chromosamal studies in a few cases showed no abno