PURPOSE OF REVIEW: Early stage lung disease has long been synonymous with infancy and childhood. As diagnosis happens earlier and conventional management improves, we are seeing larger proportions of people with cystic fibrosis (CF) in adolescence and even adulthood with well preserved lung health. The availability of highly effective cystic fibrosis transmembrane conductance regulator modulator drugs for a large proportion of the CF population will impact even further. Transitioning into adult care with 'normal' lung function will become more common. However, it is crucial that we are not blasé about this phase, which sets the scene for future lung health. It is well recognized that lung function assessed by spirometry is insensitive to 'e...
RATIONALE: Implementation of intervention strategies to prevent lung damage in early cystic fibro...
Cystic fibrosis (CF) lung disease starts early in life and progresses even in the absence of clinica...
BACKGROUND: Clinical trials in cystic fibrosis (CF) have been hindered by the paucity of well charac...
PURPOSE OF REVIEW: Early stage lung disease has long been synonymous with infancy and childhood. As ...
Purpose of review: Most treatment of newborn screening-diagnosed cystic fibrosis is not evidence-bas...
Aims: The lung clearance index (LCI) is a lung function test that can detect early cystic fibrosis (...
Structural and functional defects within the lungs of children with cystic fibrosis (CF) are detecta...
Cystic fibrosis (CF) lung disease commences early in the disease progression and is the most common ...
Background Long-term benefits of newborn screening (NBS) for cystic fibrosis (CF) have been establis...
Background Cystic fibrosis (CF) lung disease starts in infancy and can be assessed for structural lu...
Aims: To determine the relation between lower airway infection and inflammation, respiratory symp-to...
Most morbidity in cystic fibrosis (CF) is due to progressive pulmonary disease. Recently, small mole...
Cystic fibrosis (CF) is a life-shortening disease with significant morbidity. Despite overall improv...
Rationale: Pulmonary inflammation, infection, and structural lung disease occur early in life in chi...
Background: Clinical trials in cystic fibrosis (CF) have been hindered by the paucity of well charac...
RATIONALE: Implementation of intervention strategies to prevent lung damage in early cystic fibro...
Cystic fibrosis (CF) lung disease starts early in life and progresses even in the absence of clinica...
BACKGROUND: Clinical trials in cystic fibrosis (CF) have been hindered by the paucity of well charac...
PURPOSE OF REVIEW: Early stage lung disease has long been synonymous with infancy and childhood. As ...
Purpose of review: Most treatment of newborn screening-diagnosed cystic fibrosis is not evidence-bas...
Aims: The lung clearance index (LCI) is a lung function test that can detect early cystic fibrosis (...
Structural and functional defects within the lungs of children with cystic fibrosis (CF) are detecta...
Cystic fibrosis (CF) lung disease commences early in the disease progression and is the most common ...
Background Long-term benefits of newborn screening (NBS) for cystic fibrosis (CF) have been establis...
Background Cystic fibrosis (CF) lung disease starts in infancy and can be assessed for structural lu...
Aims: To determine the relation between lower airway infection and inflammation, respiratory symp-to...
Most morbidity in cystic fibrosis (CF) is due to progressive pulmonary disease. Recently, small mole...
Cystic fibrosis (CF) is a life-shortening disease with significant morbidity. Despite overall improv...
Rationale: Pulmonary inflammation, infection, and structural lung disease occur early in life in chi...
Background: Clinical trials in cystic fibrosis (CF) have been hindered by the paucity of well charac...
RATIONALE: Implementation of intervention strategies to prevent lung damage in early cystic fibro...
Cystic fibrosis (CF) lung disease starts early in life and progresses even in the absence of clinica...
BACKGROUND: Clinical trials in cystic fibrosis (CF) have been hindered by the paucity of well charac...