The structure of interstitial lung diseases in children of the first two years of life

Ovsyannikov D.Y.
Belyashova M.A.
Boytsova E.V.
Avakyan A.A.
Alekseeva O.V.
Asherova I.K.
Asherova-Yushkova D.V.
Bogdanova A.V.
Bolibok A.M.
Bronin G.O.
Valtts N.L.
Vlasova A.V.
Volkov S.N.
Volkova I.E.
Gitinov S.A.
Glazyrina A.A.
Goloborodko M.M.
Gorbunov A.V.
Grishkevich N.L.
Degtyareva E.A.
Donin I.M.
Esipenko A.P.
Zhakota D.A.
Zhdanova O.I.
Zaytseva N.O.
Zaytseva S.V.
Zapevalova E.J.
Zaharova L.A.
Ivanova N.N.
Illarionova T.Y.
Koltunov I.E.
Kondratchik K.L.
Korsunskiy A.A.
Krushelnitskiy A.A.
Krushelnitskiy A.A.
Kustova O.V.
Malinina O.V.
Marchenkov Y.V.
Nazarova T.I.
Narogan M.V.
Pavlova E.S.
Petruk N.I.
Petryaykina E.E.
Postnikova E.V.
Pugacheva I.A.
Pushkareva J.E.
Pushko L.V.
Rogatkin P.S.
Samsonovich I.R.
Semenova L.P.
Starevskaya S.V.
Stepanov O.G.
Stepanova E.V.
Suryaninova O.V.
Suslova O.V.
Turina I.E.
Usacheva O.V.
Fedorov I.A.
Fedotova O.P.
Feldfiks L.I.
Hromova A.V.
Chernyaev A.P.
Chusov K.P.
Sholtoyanu A.V.
Shokin A.A.

Publication date

March 2020

Abstract

For the first time in Russia, the article provides data on interstitial lung diseases structure in children of the first two years of life, based on a series of observations of 68 patients with these rare diseases, as a part of multi-center ambispective study. Interstitial lung diseases in observed children included: Wilson-Mikity syndrome (23,4%), neuroendocrine hyperplasia of infancy (22%), bronchiolitis obliterans with organizing pneumonia (7,4%), primary pulmonary hypoplasia (1,5%), secondary pulmonary hypoplasia with Jeune syndrome (10,3%), secondary pulmonary hypoplasia with Edwards syndrome (2,9%), secondary pulmonary hypoplasia with other associated pathology (omphalocele - 1,5%, non-immune fetal hydrops - 1,5%), subpleural cysts in...