Sturge Weber Syndrome (Encephalotrigeminal angiomatosis)

Sturge Weber Syndrome (Encephalotrigeminal angiomatosis); Color of the retina is deep red (sometimes called tomato catsup) due to a four fold thickening of the choroidal vascular bed. Optic disc is cupped due to elevated intraocular pressure. (Secondary glaucoma) Patient had a major ""port wine"" malformation on the right forehead. These patients have superficial cerebral angiomatoses with cortical calcification. Right eye. Pair with R1_B1bChoroidDiffuse choroidal hemangioma; GlaucomaPort wine hemangioma of the fac