Bilateral Orbital Masses with Uzun Kemikler (X-Ray)

Left-sided periorbital headache; Retroorbital pain OD with rednessA 51-year old male with progressive left-sided periorbital headhache and retroorbital eye pain with redness. Previous history significant for hypertension, diabetes mellitus, amblyopia OD and rhinoplasty.VA: 20/80 OD; 20/25 OS; Color plates: 10/11 OU; RAPD OD; Tonometry: 11 OD, 15 OSCT; MRIDiffuse xanthogranulomatous inflammation with lymphocytic and plasmacytic collections.Antineoplastic agents1. Franzius C, Sciuk J, Bremer C, Kempkes M, Schober O. Determination of extent and activity with radionuclide imaging in Erdheim-Chester disease. Clinical Nuclear Medicine 1999; 24(4): 252-5. 2. Shields JA, Karcioglu ZA, Shields CL, Eagle RC, Wong S. Orbital and eyelid involvement with Erdheim-Chester disease. A report of two cases. Arch-Ophthalmol 1991 June;109(6):850-4. 3. Wright RA, Hermann RC, Parisi JE. Neurological manifestations of Erdheim-Chester disease. J Neurol- Neurosurg-Psychiatry 1999 Jan;66(1): 72-5. 4. Valmaggia C, Neuweiler J, Fretz C, Gottlob I. A case of Erdheim-Chester disease with orbital involvement. Arch-Ophthalmol 1997 Nov; 115(11): 1467-8. 5. Caparros Lefebvre D, Pruyo JP, Remy M, Wallaert B, Petit H. Neuroradiologic aspects of Chester- Erdheim disease. American Journal of Neuroradiology 1995 Apr; 16(4): 735-40. 6. Miller RL, Sheeler LR, Bauer TW, Bukowski RM. Erdheim-Chester disease. Case report and review of the literature. American Journal of Medicine 1986 Jun; 80(6): 1230-6. 7. Veyssier-Beot C, Cacoub P, et al. Erdheim Chester disease. Clinical and radiologic characteristics of 59 cases. Medicine (Baltimore) 1996 May; 75