What's In a Name? (Presentation Video)

Ptosis; impaired eye movements; headache; forehead numbness76-year old male; five year history of muscle pain and arthralgia; four year history of PMR symptoms; gastrointestinal illness.20/20-2 in the right side, light perception in the left side.CT; MRIIntraconal mass which demonstrated heterogeneous enhancement and appeared to extend to the optic canal; an extensive necrotizing process with palisading histiocytes and multinucleate giant cells with an inflammatory infiltrate, including neutrophils, lymphocytes, and plasma cellsLow dose steroids; Mycophenolate1. Woo T, Francis I, Wilcsek G, et al. Australasian Orbital and Adnexal Wegener's Granulomatosis. Ophthalmology 108(9): 1535-1542, 2001. 2. Ahmed M, Niffenegger J, Jakobiec F, et al. Diagnosis of limited ophthalmic Wegener Granulomatosis: distinctive pathologic features with ANCA test confirmation. Int Ophthalmol 28:35-46, 2008. 3. Harman L, Margo C. Wegener's Granulomatosis. Survey of Ophthalmology 42: 458-480, 1998. 4. Rao J, Weinberger M, Oddone E. The Role of Antineutrophil Cytoplasmic Antibody (c-ANCA) Testing in the Diagnosis of Wegener Granulomatosis. Annals of Internal Medicine 123:925-932, 1995kbdwegenergranulomatosi