Add to ORKGCongenital acinar dysplasia is a lethal, developmental lung malformation resulting in neonatal respiratory insufficiency. This entity is characterized by pulmonary hypoplasia and arrest in the pseudoglandular stage of development, resulting in the absence of functional gas exchange. The etiology is unknown, but a relationship with the disruption of the TBX4-FGF10 pathway has been described. There are no definitive antenatal diagnostic tests. It is a diagnosis of exclusion from other diffuse embryologic lung abnormalities with identical clinical presentations that are, however, histopathologically distinct
Congenital lung lesions comprise a broad spectrum of rate but clinically significant developmental a...
Prenatal diagnosis of congenital lung anomalies has increased in recent years as imaging methods hav...
Congenital cystic adenomatoid malformation of the lung is a rare lesion that typically manifests as ...
Objective - Describe a case of congenital acinar dysplasia and review the literature. Study Desig...
Congenital pulmonary airway malformation (CPAM) is a developmental malformation of the lower respira...
Congenital pulmonary malformations should be considered in the list of differential diagnoses for pr...
Purpose: The aim of the study was to review the authors' experience with alveolar capillary dysplasi...
Alveolar capillary dysplasia with misalignment of pulmonary veins (ACD/MPV) is a rare, developmental...
Misalignment of lung vessels (MLV) with or without alveolar capillary dysplasia (ACD) is a rare caus...
International audiencePrimary defects in lung branching morphogenesis, resulting in neonatal lethal ...
Congenital cystic adenomatoid malformation (CCAM) is an hamartomatous congenital pulmonary airway ma...
Congenital lung lesions comprise a broad spectrum of rare but clinically significant developmental a...
Congenital lung lesions comprise a broad spectrum of rate but clinically significant developmental a...
Prenatal diagnosis of congenital lung anomalies has increased in recent years as imaging methods hav...
Congenital cystic adenomatoid malformation of the lung is a rare lesion that typically manifests as ...
Objective - Describe a case of congenital acinar dysplasia and review the literature. Study Desig...
Congenital pulmonary airway malformation (CPAM) is a developmental malformation of the lower respira...
Congenital pulmonary malformations should be considered in the list of differential diagnoses for pr...
Purpose: The aim of the study was to review the authors' experience with alveolar capillary dysplasi...
Alveolar capillary dysplasia with misalignment of pulmonary veins (ACD/MPV) is a rare, developmental...
Misalignment of lung vessels (MLV) with or without alveolar capillary dysplasia (ACD) is a rare caus...
International audiencePrimary defects in lung branching morphogenesis, resulting in neonatal lethal ...
Congenital cystic adenomatoid malformation (CCAM) is an hamartomatous congenital pulmonary airway ma...
Congenital lung lesions comprise a broad spectrum of rare but clinically significant developmental a...
Congenital lung lesions comprise a broad spectrum of rate but clinically significant developmental a...
Prenatal diagnosis of congenital lung anomalies has increased in recent years as imaging methods hav...
Congenital cystic adenomatoid malformation of the lung is a rare lesion that typically manifests as ...