49,XXXXY Syndrome Dental Treatment: a Case Report

This paper presents a 12-year-old male patient with XXXXY syndrome, who was treated under general anesthesia twice due to mental retardation and uncooperative behavior. The general and dentofacial manifestations of XXXXY syndrome where present.The child had to be treated as as an emergency case both times due to severe pain and abcesses. Several teeth were severely decayed and had to be extracted that led to severe anodontia as there were no secondary dentition to follow. This case emphasises the importance of regular dental care, good nutricion and monitoring of dental development in children with XXXXY syndrome. Key-words: XXXXY syndrome,dentofacial manifestations,dental car