Síndrome de Sjögren. Reporte de dos casos y revisión de la literatura

Introduction: the Sjögren syndrome is an autoimmune disease; this means that the immune system attacks its own cells. The immune system attacks the glands that produce secretions and humidity causing dryness in the mouth and in the eyes, other parts of the body can be affected causing a variety of possible symptoms.Case presentation: it was presented a 12 year- old- masculine patient, of rural origin (Jiguaní), white race, with 4 month antecedents before the hospitalization with a volume increase in the right pre auricular region, with eye dryness symptoms and little saliva, who was hospitalized on April 12, 2010, to be surgically treated on April 13, and a 22 feminine patient of rural origin with repeated antecedents of parotitis, keratoconjunctivitis, dry mouth and occasional articular pains, with a facial paralysis; remaining like a sequel the paralysis of the inferior facial branch. Both patients presented a Primary and Secondary Syndrome of Sjögren.Discussion: recently it has been recognized an entity, similar to the SS: the syndrome of infiltrating diffuse Lymphocytosis (SIDL), but is affects preferably to masculine patients infected with the HIV, the lymphocytes participants are of type CD8, instead of CD4 as it occurs in the SS.Conclusions: both patients were surgically treated and they keep their treatments with the Otolaryngology, Ophthalmology and Rheumatology services. According to the symptoms of the patients and the physical examination, the child was considered a Primary Sjogren Syndrome (PSS) and to the youngster was considered a Secondary Sjogren Syndrome (SSS).Se presenta a un paciente masculino, de 12 años de edad, procedencia rural (Jiguaní), raza blanca, con antecedentes de 4meses antes del ingreso con aumento de volumen en la región preauricular derecha, con síntomas de sequedad en los ojos y poca saliva, que es ingresado el día 12 de abril del año 2010 para ser intervenido quirúrgicamente el día 13 de abril y una paciente femenina de 22 años, procedencia rural con historia de parotiditis a repetición, queratoconjuntivitis, boca seca y dolores articulares ocasionales, así como una parálisis facial quedando como secuela parálisis de la rama inferior del facial. Ambos pacientes, histológicamente presentaron un Síndrome de Sjögren primario y secundario, respectivamente.