Complex double-outlet right ventricle repair in a neonate with complete tracheal agenesis.

Tracheal agenesis is a rare malformation with fatal consequences in very early life. We report the case of a baby girl with tracheal agenesis who during early infancy underwent complete repair of her associated {S,D,D} double-outlet right ventricle with supracardiac total anomalous pulmonary venous connection and is still alive at the age of 10 months