Sacrococcygeal chordoma presenting as a retro rectal tumour

AbstractINTRODUCTIONChordomas are rare, slow growing, locally destructive bone tumours arising from the notochord.PRESENTATION OF CASEPresenting a case of a 65 year old man, who presented with complaints of swelling on the right lower back for 1 year associated with pain.On, physical examination, a swelling measuring 5cm×4cm was noted in the lower back with posterior wall indentation on per rectal examination.MRI revealed a mass lesion involving the sacrum (s3–s4) and coccyx. FNAC showed features of a chroma.At surgery, we excised a mass from the retrorectal space and biopsy proved it to be a chondroid chordoma, a variant of chordoma.DISCUSSIONChordomas are solid malignant tumours that arise from vestiges of the foetal notochord. Common locations are the clivus and the sacrococcygeus region.Annual incidence of these tumours is 1 in one million. MRI is the imaging modality of choice. Prognosis improves based on the age, resected margins and postoperative treatment.CONCLUSIONHere, we shall discuss the literature, variants, treatment and prognosis of this rare tumour