Add to ORKGThe article is devoted to specific disorders of the respiratory system in cystic fibrosis. 64 patients with cystic fibrosis (CF) aged 2 months to 32 years and residing in the Udmurtian Republic were studied. Epidemiological and genetic specifics of this disease in the mentioned region of the RF were examined. Clinical, X-ray, functional and microbiological studies of the CF patients’ respiratory system were conducted. It was found that genotype delF508 and chronic infection Pseudomonas aeruginosa, Staphylococcus aureus cause severe structural changes to the bronchopulmonary system more often. The obtained data suggest the advisability of identifying the groups of CF patients at the highest risk of severe respiratory system disorders in orde...
Relevance. Life expectancy of cystic fibrosis patients mostly depends on the degree of respiratory s...
The work is devoted to the study of the clinical and paraclinical peculiarities in children with CF ...
OBJECTIVE: To describe the clinical impact of the first year treatment with dornase alfa, according...
The article is devoted to specific disorders of the respiratory system in cystic fibrosis. 64 patien...
CFTR protein (cystic fibrosis trans membrane conductance regulator) is expressed in multiple epithel...
Cystic fibrosis (CF) is a complex, systemic autosomal recessive disease that affects the functions o...
As part of a study was a group of children born between 1993-2005 with the diagnostic of cystic fibr...
<p><em>The center for diagnostic, treatment, rehabilitation and social adaptation of patients with c...
Dornase alpha plays an important role in the basic treatment of cystic fibrosis, having three clinic...
Cystic Fibrosis (CF) is a lethal disease affecting children, adolescents and mature adults. However,...
Cystic fibrosis (CF) is the most common severe autosomal recessive disorder among Caucasians and is ...
Pulmonary infections in cystic fibrosis In cystic fibrosis (CF), the genetic defect of the cystic fi...
The theme of this thesis is children´s cystic fibrosis and the impact of using the methods of physio...
textabstractCystic fibrosis (CF) is the most common single gene disorder in The Netherlands and occu...
AbstractCystic fibrosis (CF) is the most common autosomal recessive genetic disease caused by mutati...
Relevance. Life expectancy of cystic fibrosis patients mostly depends on the degree of respiratory s...
The work is devoted to the study of the clinical and paraclinical peculiarities in children with CF ...
OBJECTIVE: To describe the clinical impact of the first year treatment with dornase alfa, according...
The article is devoted to specific disorders of the respiratory system in cystic fibrosis. 64 patien...
CFTR protein (cystic fibrosis trans membrane conductance regulator) is expressed in multiple epithel...
Cystic fibrosis (CF) is a complex, systemic autosomal recessive disease that affects the functions o...
As part of a study was a group of children born between 1993-2005 with the diagnostic of cystic fibr...
<p><em>The center for diagnostic, treatment, rehabilitation and social adaptation of patients with c...
Dornase alpha plays an important role in the basic treatment of cystic fibrosis, having three clinic...
Cystic Fibrosis (CF) is a lethal disease affecting children, adolescents and mature adults. However,...
Cystic fibrosis (CF) is the most common severe autosomal recessive disorder among Caucasians and is ...
Pulmonary infections in cystic fibrosis In cystic fibrosis (CF), the genetic defect of the cystic fi...
The theme of this thesis is children´s cystic fibrosis and the impact of using the methods of physio...
textabstractCystic fibrosis (CF) is the most common single gene disorder in The Netherlands and occu...
AbstractCystic fibrosis (CF) is the most common autosomal recessive genetic disease caused by mutati...
Relevance. Life expectancy of cystic fibrosis patients mostly depends on the degree of respiratory s...
The work is devoted to the study of the clinical and paraclinical peculiarities in children with CF ...
OBJECTIVE: To describe the clinical impact of the first year treatment with dornase alfa, according...