Cochlear Nerve Agenesis in Unilateral Auditory Neuropathy Spectrum Disorder: Case Report

Unilateral auditory neuropathy spectrum disorder (U-ANSD) is characterized by abnormal audiological findings such as abnormal or absent auditory brainstem response with normal otoacoustic emissions in one ear. Some cases with U-ANSD might have cochlear nerve agenesis or dysplasia. In this case report, we represent a case with U-ANSD and cochlear agenesis.