Multifocal occurrence of extra-abdominal desmoid type fibromatosis – A rare manifestation. A clinicopathological study of 6 sporadic cases and 1 hereditary case
- Bekers, E.M. (Elise)
- Broekhoven, D.L.M. (Danique) van
- Dalen, T. (Thijs) van
- Bonenkamp, J.J. (Han)
- van der Geest, I.C.M. (Ingrid C.M.)
- Rooy, J.W.J. (Jacky) de
- Gorp, J. (Joost) van
- Creytens, D.H. (David H.)
- Leng, W.W.J. (Wendy) de
- Scheijen, B. (Blanca)
- Eijkelenboom, A. (Astrid)
- Flucke, U.E. (Uta )
DOIAbstract
Desmoid-type fibromatosis, also called desmoid tumor, is a locally aggressive myofibroblastic neoplasm that usually arises in deep soft tissue with significant potential for local recurrence. It displays an unpredictable clinical course. β-Catenin, the genetic key player of desmoid tumors shows nuclear accumulation due to mutations that preve
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