Contains fulltext : 50524.pdf (publisher's version ) (Closed access)The final steps in the production of adenosine triphosphate (ATP) in mitochondria are executed by a series of multisubunit complexes and electron carriers, which together constitute the oxidative phosphorylation (OXPHOS) system. OXPHOS is under dual genetic control, with communication between the nuclear and mitochondrial genomes essential for optimal assembly and function of the system. We describe the current understanding of the metabolic consequences of pathological OXPHOS defects, based on analyses of patients and of genetically engineered model systems. Understanding the metabolic consequences of OXPHOS disease is of key importance for elucidating pa...
Abstract. Different tissues display distinct sensitivities to defective mitochondrial oxidative phos...
Mitochondrial disorders are a heterogeneous group of often multisystemic and early fatal diseases, w...
Contains fulltext : 153405.pdf (publisher's version ) (Closed access)While often p...
The final steps in the production of adenosine triphosphate (ATP) in mitochondria are executed by a ...
The final steps in the production of adenosine triphosphate (ATP) in mitochondria are executed by a ...
Contains fulltext : 88978.pdf (publisher's version ) (Open Access)Mitochondrial di...
Contains fulltext : 19614__asseofthh.pdf (publisher's version ) (Open Access)Mitoc...
The final steps in the production of adenosine triphosphate (ATP) in mitochondria are executed by a ...
Item does not contain fulltextThe mitochondrial oxidative phosphorylation (OXPHOS) system is the fin...
Contains fulltext : 89702.pdf (publisher's version ) (Closed access)Mitochondrial ...
Contains fulltext : 81397.pdf (publisher's version ) (Closed access)The cellular c...
Contains fulltext : 70146.pdf (publisher's version ) (Open Access)Oxidative phosph...
Contains fulltext : 83310.pdf (publisher's version ) (Closed access)Combined oxida...
Contains fulltext : 88552.pdf (publisher's version ) (Closed access)Combined oxida...
Contains fulltext : 79627.pdf (publisher's version ) (Closed access)Research of pa...
Abstract. Different tissues display distinct sensitivities to defective mitochondrial oxidative phos...
Mitochondrial disorders are a heterogeneous group of often multisystemic and early fatal diseases, w...
Contains fulltext : 153405.pdf (publisher's version ) (Closed access)While often p...
The final steps in the production of adenosine triphosphate (ATP) in mitochondria are executed by a ...
The final steps in the production of adenosine triphosphate (ATP) in mitochondria are executed by a ...
Contains fulltext : 88978.pdf (publisher's version ) (Open Access)Mitochondrial di...
Contains fulltext : 19614__asseofthh.pdf (publisher's version ) (Open Access)Mitoc...
The final steps in the production of adenosine triphosphate (ATP) in mitochondria are executed by a ...
Item does not contain fulltextThe mitochondrial oxidative phosphorylation (OXPHOS) system is the fin...
Contains fulltext : 89702.pdf (publisher's version ) (Closed access)Mitochondrial ...
Contains fulltext : 81397.pdf (publisher's version ) (Closed access)The cellular c...
Contains fulltext : 70146.pdf (publisher's version ) (Open Access)Oxidative phosph...
Contains fulltext : 83310.pdf (publisher's version ) (Closed access)Combined oxida...
Contains fulltext : 88552.pdf (publisher's version ) (Closed access)Combined oxida...
Contains fulltext : 79627.pdf (publisher's version ) (Closed access)Research of pa...
Abstract. Different tissues display distinct sensitivities to defective mitochondrial oxidative phos...
Mitochondrial disorders are a heterogeneous group of often multisystemic and early fatal diseases, w...
Contains fulltext : 153405.pdf (publisher's version ) (Closed access)While often p...