Syndrome de Bannayan-Zonana d’évolution fatale

Bannayan-Zonana syndrome is a rare entity characterized by macro-\ud cephaly and multiple soft tissue and visceral hamartomas and\ud lipomas. Knowledge of this syndrome is important given the risk\ud of sometimes fatal bleeding and visceral neoplasia in adulthood. We\ud report on a new case, original in its sporadic occurrence and rapidly\ud fatal progression