Additional file 2: of Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo− mouse model of FKRP-deficient muscular dystrophy

Additional file 3: of Four-week rapamycin treatment improves muscular dystrophy in a fukutin-deficient mouse model of dystroglycanopathy

Steven Foltz (3543443)
Junna Luan (845138)
Jarrod Call (3543437)
Ankit Patel (774246)
Kristen Peissig (3543440)
Marisa Fortunato (3543446)
Aaron Beedle (3543434)

June 2016

(A) Fold-change over background values for pro-inflammatory cytokines (IL-1Î˛, MCP-1, and TNF-Îą) te...

Additional file 6: of Defects in sarcolemma repair and skeletal muscle function after injury in a mouse model of Niemann-Pick type A/B disease

V. Michailowsky (6177458)
H. Li (1597072)
B. Mittra (6177461)
S. Iyer (1407712)
D. Mazรกla (6177497)
M. Corrotte (6177467)
Y. Wang (473169)
E. Chin (6177470)
R. Lovering (5090585)
N. Andrews (6177473)

January 2019

Table S5. Master proteins from a skeletal muscle subset significantly up- or downregulated in QF, FD...

Additional file 2: Figure S1. of Deletion of the Ste20-like kinase SLK in skeletal muscle results in a progressive myopathy and muscle weakness

Benjamin Pryce (3714709)
Khalid Al-Zahrani (3714706)
Sébastien Dufresne (3714718)
Natalya Belkina (3714715)
Cédrik Labrèche (3714712)
Genaro Patino-Lopez (2432215)
Jérôme Frenette (796421)
Stephen Shaw (37225)
Luc Sabourin (3714703)

February 2017

SLK knockout mice display reduced body mass, muscle size, but show no increase in fibrosis. (A) Body...

Additional file 3: of Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo− mouse model of FKRP-deficient muscular dystrophy

Qing Yu (337275)
Melissa Morales (5072570)
Ning Li (45258)
Alexander Fritz (5072582)
Ren Ruobing (5072579)
Anthony Blaeser (3202620)
Ershia Francois (5072576)
Qi-Long Lu (3202617)
Kanneboyina Nagaraju (241056)
Christopher Spurney (5072573)

April 2018

Table S2. Histological analyses of the diaphragm in P448Lneo− (FKRP) and control (BL6) mice at 1, 2,...

Additional file 4: of Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo− mouse model of FKRP-deficient muscular dystrophy

Qing Yu (337275)
Melissa Morales (5072570)
Ning Li (45258)
Alexander Fritz (5072582)
Ren Ruobing (5072579)
Anthony Blaeser (3202620)
Ershia Francois (5072576)
Qi-Long Lu (3202617)
Kanneboyina Nagaraju (241056)
Christopher Spurney (5072573)

April 2018

Table S3. Echocardiography results for P448Lneo− (FKRP) and control (BL6) mice at 2, 6, and 9 months...

Additional file 1: of Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo− mouse model of FKRP-deficient muscular dystrophy

Qing Yu (337275)
Melissa Morales (5072570)
Ning Li (45258)
Alexander Fritz (5072582)
Ren Ruobing (5072579)
Anthony Blaeser (3202620)
Ershia Francois (5072576)
Qi-Long Lu (3202617)
Kanneboyina Nagaraju (241056)
Christopher Spurney (5072573)

April 2018

Figure S1. Behavioral activity monitoring in P448Lneo− (FKRP), exercised P448Lneo− (FKRP-treadmill),...

Additional file 1: of GRAF1 deficiency blunts sarcolemmal injury repair and exacerbates cardiac and skeletal muscle pathology in dystrophin-deficient mice

Kaitlin Lenhart (3442547)
Thomas OâNeill (3442568)
Zhaokang Cheng (3442565)
Rachel Dee (3442550)
Alexis Demonbreun (3442562)
Jianbin Li (312148)
Xiao Xiao (99147)
Elizabeth McNally (358926)
Christopher Mack (3442553)
Joan Taylor (3442556)

August 2015

Figure S1. TEM of GRAF1 tibialis anterior muscle. TEM (Ă2500 magnification) reveals T-tubule abnorm...

Additional file 2: of Late-onset megaconial myopathy in mice lacking group I Paks

Giselle Joseph (6389681)
Margaret Hung (6389684)
Aviva Goel (258607)
Mingi Hong (129953)
Marysia-Kolbe Rieder (6389687)
Noam Beckmann (4575562)
Madhavika Serasinghe (6389690)
Jerry Chipuk (6389693)
Parvathi Devarakonda (6389696)
David Goldhamer (6389699)
Paulina Aldana-Hernandez (6389702)
Jonathan Curtis (3766723)
RenĂŠ Jacobs (6389711)
Robert Krauss (442384)

February 2019

Figure S2. Young adult dKO mice show limited signs of muscle disease. H&E-stained sections of uninju...

Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo− mouse model of FKRP-deficient muscular dystrophy

Qing Yu
Melissa Morales
Ning Li
Alexander G. Fritz
Ren Ruobing
Anthony Blaeser
Ershia Francois
Qi-Long Lu
Kanneboyina Nagaraju
Christopher F. Spurney

April 2018

Abstract Background Fukutin-related protein (FKRP) mutations are the most common cause of dystroglyc...

Additional file 2: of Klotho expression is a prerequisite for proper muscle stem cell function and regeneration of skeletal muscle

Hellen Ahrens (5482466)
Judith Huettemeister (5482469)
Manuel Schmidt (12990)
Christoph Kaether (3539447)
Julia von Maltzahn (313864)

July 2018

Figure S2. Fiber types are not changed in ΔKlotho mice. (A) Representative immunofluorescence staini...

Additional file 1: of Klotho expression is a prerequisite for proper muscle stem cell function and regeneration of skeletal muscle

Hellen Ahrens (5482466)
Judith Huettemeister (5482469)
Manuel Schmidt (12990)
Christoph Kaether (3539447)
Julia von Maltzahn (313864)

July 2018

Figure S1. ΔKlotho mice display signs of sarcopenia. (A) Immunofluorescence of cross-sections of TA ...

Additional file 2: Figure S1. of Increased plasma lipid levels exacerbate muscle pathology in the mdx mouse model of Duchenne muscular dystrophy

Nadia Milad (4431331)
Zoe White (3506846)
Arash Tehrani (4431328)
Stephanie Sellers (57317)
Fabio Rossi (400530)
Pascal Bernatchez (152801)

September 2017

Plasma lipid levels at 4 months of age on Western diet. Plasma CK in IU/L (A), total cholesterol in ...

Additional file 1: of Genetic deletion of muscle RANK or selective inhibition of RANKL is not as effective as full-length OPG-fc in mitigating muscular dystrophy

Sébastien Dufresne (3714718)
Antoine Boulanger-Piette (5148089)
Sabrina Bossé (5148098)
Anteneh Argaw (443820)
Dounia Hamoudi (3629165)
Laetitia Marcadet (5148092)
Daniel Gamu (497886)
Val Fajardo (5148095)
Hideo Yagita (109170)
Josef Penninger (5148086)
A. Russell Tupling (428971)
Jérôme Frenette (796421)

April 2018

Table 1. All treatments and muscle-specific genetic deletion of RANK did not have an impact on muscl...

Additional file 4: of Four-week rapamycin treatment improves muscular dystrophy in a fukutin-deficient mouse model of dystroglycanopathy

Steven Foltz (3543443)
Junna Luan (845138)
Jarrod Call (3543437)
Ankit Patel (774246)
Kristen Peissig (3543440)
Marisa Fortunato (3543446)
Aaron Beedle (3543434)

June 2016

Tissue mass-normalized values of cytochrome C reduced in vitro by succinate dehydrogenase from homog...

Additional file 1: Figure S8. of Increased plasma lipid levels exacerbate muscle pathology in the mdx mouse model of Duchenne muscular dystrophy

Nadia Milad (4431331)
Zoe White (3506846)
Arash Tehrani (4431328)
Stephanie Sellers (57317)
Fabio Rossi (400530)
Pascal Bernatchez (152801)

September 2017

Muscle and cardiac data stratified at 7 months on Western diet stratified by gender. WT (n = 5M, 4F)...

Additional file 3: of Four-week rapamycin treatment improves muscular dystrophy in a fukutin-deficient mouse model of dystroglycanopathy

Steven Foltz (3543443)
Junna Luan (845138)
Jarrod Call (3543437)
Ankit Patel (774246)
Kristen Peissig (3543440)
Marisa Fortunato (3543446)
Aaron Beedle (3543434)

June 2016

(A) Fold-change over background values for pro-inflammatory cytokines (IL-1Î˛, MCP-1, and TNF-Îą) te...

Additional file 6: of Defects in sarcolemma repair and skeletal muscle function after injury in a mouse model of Niemann-Pick type A/B disease

V. Michailowsky (6177458)
H. Li (1597072)
B. Mittra (6177461)
S. Iyer (1407712)
D. Mazรกla (6177497)
M. Corrotte (6177467)
Y. Wang (473169)
E. Chin (6177470)
R. Lovering (5090585)
N. Andrews (6177473)

January 2019

Table S5. Master proteins from a skeletal muscle subset significantly up- or downregulated in QF, FD...

Additional file 2: Figure S1. of Deletion of the Ste20-like kinase SLK in skeletal muscle results in a progressive myopathy and muscle weakness

Benjamin Pryce (3714709)
Khalid Al-Zahrani (3714706)
Sébastien Dufresne (3714718)
Natalya Belkina (3714715)
Cédrik Labrèche (3714712)
Genaro Patino-Lopez (2432215)
Jérôme Frenette (796421)
Stephen Shaw (37225)
Luc Sabourin (3714703)

February 2017

SLK knockout mice display reduced body mass, muscle size, but show no increase in fibrosis. (A) Body...

Additional file 3: of Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo− mouse model of FKRP-deficient muscular dystrophy

Qing Yu (337275)
Melissa Morales (5072570)
Ning Li (45258)
Alexander Fritz (5072582)
Ren Ruobing (5072579)
Anthony Blaeser (3202620)
Ershia Francois (5072576)
Qi-Long Lu (3202617)
Kanneboyina Nagaraju (241056)
Christopher Spurney (5072573)

April 2018

Table S2. Histological analyses of the diaphragm in P448Lneo− (FKRP) and control (BL6) mice at 1, 2,...

Additional file 4: of Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo− mouse model of FKRP-deficient muscular dystrophy

Qing Yu (337275)
Melissa Morales (5072570)
Ning Li (45258)
Alexander Fritz (5072582)
Ren Ruobing (5072579)
Anthony Blaeser (3202620)
Ershia Francois (5072576)
Qi-Long Lu (3202617)
Kanneboyina Nagaraju (241056)
Christopher Spurney (5072573)

April 2018

Table S3. Echocardiography results for P448Lneo− (FKRP) and control (BL6) mice at 2, 6, and 9 months...

Additional file 1: of Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo− mouse model of FKRP-deficient muscular dystrophy

Qing Yu (337275)
Melissa Morales (5072570)
Ning Li (45258)
Alexander Fritz (5072582)
Ren Ruobing (5072579)
Anthony Blaeser (3202620)
Ershia Francois (5072576)
Qi-Long Lu (3202617)
Kanneboyina Nagaraju (241056)
Christopher Spurney (5072573)

April 2018

Figure S1. Behavioral activity monitoring in P448Lneo− (FKRP), exercised P448Lneo− (FKRP-treadmill),...

Additional file 1: of GRAF1 deficiency blunts sarcolemmal injury repair and exacerbates cardiac and skeletal muscle pathology in dystrophin-deficient mice

Kaitlin Lenhart (3442547)
Thomas OâNeill (3442568)
Zhaokang Cheng (3442565)
Rachel Dee (3442550)
Alexis Demonbreun (3442562)
Jianbin Li (312148)
Xiao Xiao (99147)
Elizabeth McNally (358926)
Christopher Mack (3442553)
Joan Taylor (3442556)

August 2015

Figure S1. TEM of GRAF1 tibialis anterior muscle. TEM (Ă2500 magnification) reveals T-tubule abnorm...

Additional file 2: of Late-onset megaconial myopathy in mice lacking group I Paks

Giselle Joseph (6389681)
Margaret Hung (6389684)
Aviva Goel (258607)
Mingi Hong (129953)
Marysia-Kolbe Rieder (6389687)
Noam Beckmann (4575562)
Madhavika Serasinghe (6389690)
Jerry Chipuk (6389693)
Parvathi Devarakonda (6389696)
David Goldhamer (6389699)
Paulina Aldana-Hernandez (6389702)
Jonathan Curtis (3766723)
RenĂŠ Jacobs (6389711)
Robert Krauss (442384)

February 2019

Figure S2. Young adult dKO mice show limited signs of muscle disease. H&E-stained sections of uninju...

Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo− mouse model of FKRP-deficient muscular dystrophy

Qing Yu
Melissa Morales
Ning Li
Alexander G. Fritz
Ren Ruobing
Anthony Blaeser
Ershia Francois
Qi-Long Lu
Kanneboyina Nagaraju
Christopher F. Spurney

April 2018

Abstract Background Fukutin-related protein (FKRP) mutations are the most common cause of dystroglyc...

Additional file 2: of Klotho expression is a prerequisite for proper muscle stem cell function and regeneration of skeletal muscle

Hellen Ahrens (5482466)
Judith Huettemeister (5482469)
Manuel Schmidt (12990)
Christoph Kaether (3539447)
Julia von Maltzahn (313864)

July 2018

Figure S2. Fiber types are not changed in ΔKlotho mice. (A) Representative immunofluorescence staini...

Additional file 1: of Klotho expression is a prerequisite for proper muscle stem cell function and regeneration of skeletal muscle

Hellen Ahrens (5482466)
Judith Huettemeister (5482469)
Manuel Schmidt (12990)
Christoph Kaether (3539447)
Julia von Maltzahn (313864)

July 2018

Figure S1. ΔKlotho mice display signs of sarcopenia. (A) Immunofluorescence of cross-sections of TA ...

Additional file 2: Figure S1. of Increased plasma lipid levels exacerbate muscle pathology in the mdx mouse model of Duchenne muscular dystrophy

Nadia Milad (4431331)
Zoe White (3506846)
Arash Tehrani (4431328)
Stephanie Sellers (57317)
Fabio Rossi (400530)
Pascal Bernatchez (152801)

September 2017

Plasma lipid levels at 4 months of age on Western diet. Plasma CK in IU/L (A), total cholesterol in ...

Additional file 1: of Genetic deletion of muscle RANK or selective inhibition of RANKL is not as effective as full-length OPG-fc in mitigating muscular dystrophy

Sébastien Dufresne (3714718)
Antoine Boulanger-Piette (5148089)
Sabrina Bossé (5148098)
Anteneh Argaw (443820)
Dounia Hamoudi (3629165)
Laetitia Marcadet (5148092)
Daniel Gamu (497886)
Val Fajardo (5148095)
Hideo Yagita (109170)
Josef Penninger (5148086)
A. Russell Tupling (428971)
Jérôme Frenette (796421)

April 2018

Table 1. All treatments and muscle-specific genetic deletion of RANK did not have an impact on muscl...

Additional file 4: of Four-week rapamycin treatment improves muscular dystrophy in a fukutin-deficient mouse model of dystroglycanopathy

Steven Foltz (3543443)
Junna Luan (845138)
Jarrod Call (3543437)
Ankit Patel (774246)
Kristen Peissig (3543440)
Marisa Fortunato (3543446)
Aaron Beedle (3543434)

June 2016

Tissue mass-normalized values of cytochrome C reduced in vitro by succinate dehydrogenase from homog...

Additional file 1: Figure S8. of Increased plasma lipid levels exacerbate muscle pathology in the mdx mouse model of Duchenne muscular dystrophy

Nadia Milad (4431331)
Zoe White (3506846)
Arash Tehrani (4431328)
Stephanie Sellers (57317)
Fabio Rossi (400530)
Pascal Bernatchez (152801)

September 2017

Muscle and cardiac data stratified at 7 months on Western diet stratified by gender. WT (n = 5M, 4F)...

Additional file 3: of Four-week rapamycin treatment improves muscular dystrophy in a fukutin-deficient mouse model of dystroglycanopathy

Steven Foltz (3543443)
Junna Luan (845138)
Jarrod Call (3543437)
Ankit Patel (774246)
Kristen Peissig (3543440)
Marisa Fortunato (3543446)
Aaron Beedle (3543434)

June 2016

(A) Fold-change over background values for pro-inflammatory cytokines (IL-1Î˛, MCP-1, and TNF-Îą) te...

Additional file 6: of Defects in sarcolemma repair and skeletal muscle function after injury in a mouse model of Niemann-Pick type A/B disease

V. Michailowsky (6177458)
H. Li (1597072)
B. Mittra (6177461)
S. Iyer (1407712)
D. Mazรกla (6177497)
M. Corrotte (6177467)
Y. Wang (473169)
E. Chin (6177470)
R. Lovering (5090585)
N. Andrews (6177473)

January 2019

Table S5. Master proteins from a skeletal muscle subset significantly up- or downregulated in QF, FD...

Additional file 2: Figure S1. of Deletion of the Ste20-like kinase SLK in skeletal muscle results in a progressive myopathy and muscle weakness

Benjamin Pryce (3714709)
Khalid Al-Zahrani (3714706)
Sébastien Dufresne (3714718)
Natalya Belkina (3714715)
Cédrik Labrèche (3714712)
Genaro Patino-Lopez (2432215)
Jérôme Frenette (796421)
Stephen Shaw (37225)
Luc Sabourin (3714703)

February 2017

SLK knockout mice display reduced body mass, muscle size, but show no increase in fibrosis. (A) Body...

Additional file 2: of Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo− mouse model of FKRP-deficient muscular dystrophy

Abstract

Extracted data

Additional file 2: of Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo− mouse model of FKRP-deficient muscular dystrophy

Abstract

Extracted data

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