Creutzfeldt-Jakob disease death rates and deaths, United States, 1979–2006.^*

*<p>Deaths obtained from the multiple cause-of-death data for 1979–1998 are based on ICD-9 codes and those beginning in 1999 are based on ICD-10 codes with available computerized literal death certificate data. Death information was also obtained from other surveillance mechanisms. One death is missing both race and region; and one death is missing region.</p>†<p>Death rates expressed per 1,000,000 persons in corresponding group. Death rates and risk ratios are age-adjusted for total, sex, race, and region. The 95% confidence intervals (CIs) are given.</p>‡<p>p<0.001 for comparison of death rate to that of the referent group.