STATUS DYSTONICUS Study of five cases

ABSTRACT- Status Dystonicus (SD) is characterized by generalized muscle contractions in dystonic patients. We report 5 cases of SD, two of which in patients with dystonic cerebral palsy, one in a patient with prima-ry segmental dystonia, one in a patient with Hallervorden-Spatz syndrome and one in a patient with Wilson’s disease (WD). Three patients were admitted to an intensive care unit and treated with propofol and mida-zolam, and two were submitted to neurosurgical procedures (bilateral pallidotomy and bilateral pallidal deep brain stimulation). Triggering factors were identified in three patients as follows: infection, stress-induced and zinc therapy for WD. On follow-up, two patients presented with significant improvement of dystonia, whereas the other three cases the clinical picture ultimately returned to baseline pre-SD condition. KEY WORDS: ”status dystonicus”, dystonic storm, dystonia. “Status dystonicus”: estudo de cinco casos RESUMO- O “Status Dystonicus ” (SD) é uma situação clínica caracterizada por contratura muscular generali-zada em pacientes com distonias. Relatamos cinco casos de SD, que ocorreram em dois pacientes com disto-nia associada à paralisia cerebral, um paciente com distonia segmentar primária, um com síndrome de Hal