CT of the Temporal Bone in a Patient with Osteopathia Striata and Cranial Sclerosis

Summary: The authors present a case of congenital dysplasia affecting the long bones, skull, and other systems in a 7-year-old girl, with special attention to CT of the temporal bone, which showed abnormal ossicle fixation, a narrowed Eustachian canal, thickened sclerotic bone, and a small mastoid antrum and middle ear cavity. CT of the temporal bone can help one distinguish the etiologies of hearing loss associated with this disorder. Index terms: Temporal bone, computed tomography; Sclerosis, cranial Osteopathia striata (OS) with cranial sclerosis is a rare and potentially symptomatic form of OS (Voorhoeve disease), one of the sclerosing bone dysplasias that usually have few or even no clinical manifestations. In addition to long bon