Invited Review Update on Enteral Nutrition Support for Cystic Fibrosis

ABSTRACT: Cystic fibrosis (CF) is an inherited disease affecting the respiratory, gastrointestinal, hepatobiliary, and reproductive systems. Nutrition status in persons with CF is often compromised due to increased energy needs, frequent infections, pancreatic insufficiency, lung disease, or CF-related diabetes. Maintaining good nutri-tion status has been associated with better pulmonary function, reduced hospitalizations, and increased longev-ity. Nutrition support as oral supplementation (used in 37 % of the CF population) or tube feeding (used in13% of the CF population) is often required for children and adults with CF. The purpose of this update is to describe current consensus and evidence for enteral nutrition sup-port guidelines, reported complications of enteral feeding in the CF population, evidence of expected outcomes, an