Enhances Multimodal Imaging of a Successful Repair of a Case With Scimitar Syndrome

Scimitar syndrome is a rare congenital disorder with anincidence of approximately 2 per 100 000 live births.1 The hallmark of this syndrome is partial or complete anom-alous venous return from the right lung, directly into the inferior vena cava (IVC), thereby creating a left-to-right shunt.2 The syndrome is almost invariably associated with other cardiac and extracardiac abnormalities including atrial septal defects (ASD), dextrocardia, abnormal right lung lobation, and right lung hypoplasia.3 The infantile syndrome is highly associated with ASDs, ventricular septal defects, patent ductus arteriosus, coarctation, and tetralogy of Fallot.3 The abnormal venous drainage gives the characteristic radiographic appearance akin to that of a “scimitar ” (Turkish sword) with a shadow on the right side of the heart progres-sively widening as it approaches the cardiophrenic angle.