AN UNUSUAL CASE OF DIAPHYSEAL ACLASIS ARISING IN FINGERS

Diaphyseal aclasis (multiple hereditary exostoses) occurs in the bones developed in cartilage and gives rise to cartilage-capped exostoses. It usually affects the ends of the diaphyses of long bones of extremities (McKusick, 1972). Although the phalanges of the fingers may be shorter than normal, no record could be found of significant deformity. A case of digital deformity is described below. Case Report large that it had displaced the index finger radially A two-year-old girl presented with a deformed left (Figure 1). middle finger. The mother had noticed a lump on this finger about one year previously and it had slowly A general skeletal survey showed exostoses over the enlarged. The condition also affected the patient’s greater trochanters of both hips, over the left distal father, uncle and younger brother, but always in the long radius on the right medial malleolus, and over the distal bones such as radius, femur, tibia and fibula. end of the right radius near the styloid process. On examination, there were exostoses on the proximal At operation, a large bone exostosis with a cartilaginous phalanges of the left middle, right middle and ring cap was found on the antero-medial aspect of the base of fingers. The exostosis of the left middle finger was so the proximal phalanx of the left middle finger. Th