Congenital Horner Syndrome with Heterochromia Iridis Associated with Ipsilateral Internal Carotid

BackgroundzzHorner syndrome (HS), also known as Claude-Bernard-Horner syndrome or oculosympathetic palsy, comprises ipsilateral ptosis, miosis, and facial anhidrosis. Case ReportzzWe report herein the case of a 67-year-old man who presented with congeni-tal HS associated with ipsilateral hypoplasia of the internal carotid artery (ICA), as revealed by heterochromia iridis and confirmed by computed tomography (CT). ConclusionszzCT evaluation of the skull base is essential to establish this diagnosis and distin-guish aplasia from agenesis/hypoplasia (by the absence or hypoplasia of the carotid canal) or from acquired ICA obstruction as demonstrated by angiographic CT. Key Wordszz congenital horner syndrome, internal carotid artery agenesis, heterochromia iridis, computed tomography