© Trakya Üniversitesi Tıp Fakültesi Dergisi. Ekin Tıbbi Yayıncılık tarafından basılmıştır. Her hakkı saklıdır. © Medical Journal of Trakya University. Published by Ekin Medical Publishing. All rights reserved.

Aggressive fibromatosis is a rarely seen soft tissue tumor and originate principally from deep seated fascial or musculoaponeurotic structures.[1] Tumors of fibrous tissue origin (fibromatosis) in chest and mediastinum have been rarely reported in the litera-ture.[1-9] They are characterized by the proliferation of fibroblasts with no cytological evidence of malignancy and are organized in the form of fasciae. Aggressive fibromatosis are considered low-grade malignant sar-comas. Locally invasive, they tend to recur increasing morbidity or even mortality. The cause is unknown (trauma, hormonal factors, genetic anomaly).[2] Wide radical resection should be attempted whenever pos-sible. In cases of recurrences, multimodality therapies should be considered