SUMMARY

Teratomas are neoplasms originating in pluripotent cells. They are composed of a wide diversity of tissues representing all three germ cell layers. The sacrococcygeal area is the most common extragonadal site. A sacrococcygeal teratoma is the commonest teratoma presenting in the neonatal period. We present a term neonate who had a large teratoma in the sacrococcygeal region. The tumour was associated with polyhydramnios and elevated alpha-fetoprotein at birth. Enbloc resection of the tumour resulted in rapid decline in the alpha-fetoprotein. Histopathological examination of the mass confirmed the tissues of all the three germ cell layers