Multicentric Reticulohistiocytosis Resembling Dermatomyositis: A

We describe a 36 years old Chinese lady who presented with multiple painless non- pruritc papules and nodules on the hands, elbows, ear, face and feet associated with joint pains involving the knees and the small joints of the hands. She also had photo- distributed rash on the face, chest and back. Her systemic examination was normal. Other than the articular erosions in the interphalangeal joints and erosion on the patella bilaterally, all other investigations were normal or negative. The photo distributed patches and plaque lesion on the front and back of the chest with facial rash and papules on the knuckles of the hands may be mistaken for dermatomyositis. The histopathological examination revealed dermal infiltrates of multinucleated histiocytic giant cells with an eosinophilic ’ground glass ’ cytoplasm which confirmed the diagnosis of multicentric reticulohitiocytosis in our case. Multicentric reticulohistiocytosis (MR) is a rare disorder of skin with systemic granulomatous involvement of no known cause with distinct histopathology. It has been described to involve the skin, mucosa, joints and internal organs but all th