A Case of Bickerstaff's Brainstem Encephalitis with Guillain-Barré Syndrome Presenting Optic Neuropathy and Seizure

Bickerstaff's brainstem encephalitis (BBE), characterized by acute ophthalmoplegia and ataxia, often causes impaired consciousness and hyperreflexia. A 17-year-old man was admitted with an acute meningitic condition including high and neck stiffness. His condition rapidly deteriorated over 2 weeks, and he showed ophthal-moplegia, ataxia, seizure, tetraplegia, comatose mentality, and optic neuropathy. Electroencephalography showed diffuse slow waves. Visual evoked potentials showed no responses in the right eye. This is the first case of BBE with Guillain-Barré syndrome presenting with optic neuropathy and seizure. J Korean Neurol Assoc 23(3):389-391, 200